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GWAS Study

A genome-wide association study of total bilirubin and cholelithiasis risk in sickle cell anemia.

Milton JN, Sebastiani P, Solovieff N et al.

22558097 PubMed ID
GWAS Study Type
3057 Participants
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Chapter I

Publication Details

Comprehensive information about this research publication

Authors

MJ
Milton JN
SP
Sebastiani P
SN
Solovieff N
HS
Hartley SW
BP
Bhatnagar P
AD
Arking DE
DD
Dworkis DA
CJ
Casella JF
BE
Barron-Casella E
BC
Bean CJ
HW
Hooper WC
DM
DeBaun MR
GM
Garrett ME
SK
Soldano K
TM
Telen MJ
AA
Ashley-Koch A
GM
Gladwin MT
BC
Baldwin CT
SM
Steinberg MH
KE
Klings ES
Chapter II

Abstract

Summary of the research findings

Serum bilirubin levels have been associated with polymorphisms in the UGT1A1 promoter in normal populations and in patients with hemolytic anemias, including sickle cell anemia. When hemolysis occurs circulating heme increases, leading to elevated bilirubin levels and an increased incidence of cholelithiasis. We performed the first genome-wide association study (GWAS) of bilirubin levels and cholelithiasis risk in a discovery cohort of 1,117 sickle cell anemia patients. We found 15 single nucleotide polymorphisms (SNPs) associated with total bilirubin levels at the genome-wide significance level (p value <5 × 10(-8)). SNPs in UGT1A1, UGT1A3, UGT1A6, UGT1A8 and UGT1A10, different isoforms within the UGT1A locus, were identified (most significant rs887829, p = 9.08 × 10(-25)). All of these associations were validated in 4 independent sets of sickle cell anemia patients. We tested the association of the 15 SNPs with cholelithiasis in the discovery cohort and found a significant association (most significant p value 1.15 × 10(-4)). These results confirm that the UGT1A region is the major regulator of bilirubin metabolism in African Americans with sickle cell anemia, similar to what is observed in other ethnicities.

905 African American cases

Chapter III

Study Statistics

Key metrics and study information

3057
Total Participants
GWAS
Study Type
Yes
Replicated
2,152 African American cases
Replication Participants
African American or Afro-Caribbean
Ancestry
U.S.
Recruitment Country
Chapter IV

Analysis

Comprehensive review of health and genetic findings

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